Neuroblastoma accounts for nearly 8% of all childhood malignancies and is the most common solid tumour in children not arising from the brain.[10]Ward E, DeSantis C, Robbins A, et al. Childhood and adolescent cancer statistics, 2014. CA Cancer J Clin. 2014 Mar-Apr;64(2):83-103.
http://onlinelibrary.wiley.com/doi/10.3322/caac.21219/full
http://www.ncbi.nlm.nih.gov/pubmed/24488779?tool=bestpractice.com
[11]Stiller CA, Parkin DM. International variations in the incidence of neuroblastoma. Int J Cancer. 1992 Oct 21;52(4):538-43.
http://www.ncbi.nlm.nih.gov/pubmed/1399133?tool=bestpractice.com
In the US, incidence is approximately 8 per million persons (based on 2003-2019 data).[12]Campbell K, Siegel DA, Umaretiya PJ, et al. A comprehensive analysis of neuroblastoma incidence, survival, and racial and ethnic disparities from 2001 to 2019. Pediatr Blood Cancer. 2024 Jan;71(1):e30732.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11018254
http://www.ncbi.nlm.nih.gov/pubmed/37867409?tool=bestpractice.com
About 800 new cases are reported each year; median age at diagnosis is 17 months.[12]Campbell K, Siegel DA, Umaretiya PJ, et al. A comprehensive analysis of neuroblastoma incidence, survival, and racial and ethnic disparities from 2001 to 2019. Pediatr Blood Cancer. 2024 Jan;71(1):e30732.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11018254
http://www.ncbi.nlm.nih.gov/pubmed/37867409?tool=bestpractice.com
ACS: key statistics about neuroblastoma
Opens in new window The majority of neuroblastoma cases occur in children ≤4 years of age (34% in children <1 year; 49.9% in those aged 1-4 years).[12]Campbell K, Siegel DA, Umaretiya PJ, et al. A comprehensive analysis of neuroblastoma incidence, survival, and racial and ethnic disparities from 2001 to 2019. Pediatr Blood Cancer. 2024 Jan;71(1):e30732.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11018254
http://www.ncbi.nlm.nih.gov/pubmed/37867409?tool=bestpractice.com
While overall incidence of neuroblastoma appears to be stable in the US, small but significant increases in annual incidence have been reported among children aged 5-9 years and adolescents aged 15-19 years (average annual percent change [AAPC] 2.4% and 3.3%, respectively; 2003-2019 data).[12]Campbell K, Siegel DA, Umaretiya PJ, et al. A comprehensive analysis of neuroblastoma incidence, survival, and racial and ethnic disparities from 2001 to 2019. Pediatr Blood Cancer. 2024 Jan;71(1):e30732.
https://pmc.ncbi.nlm.nih.gov/articles/PMC11018254
http://www.ncbi.nlm.nih.gov/pubmed/37867409?tool=bestpractice.com
Rarely, neuroblastoma can be detected by ultrasound before birth.