History and exam

Key diagnostic factors

common

neck stiffness

Hemorrhagic stroke can frequently give rise to neck stiffness. Most commonly seen with subarachnoid hemorrhage due to blood causing meningeal irritation.

history of atrial fibrillation

While not a risk per se, patients with atrial fibrillation are often treated with warfarin and other direct thrombin inhibitors, increasing the likelihood of brain hemorrhage.

history of liver disease

May impair coagulation processes, leading to hemorrhage.

visual changes

Hemianopia may result from hemorrhage in the visual pathways, including the occipital lobe.

Diplopia may result from brain stem hemorrhage.

photophobia

Hemorrhagic stroke can often cause the patient to report photophobia.

sudden onset followed by progression

Intracranial hemorrhage symptoms often start suddenly and progress over several minutes.

Symptoms of ischemic stroke may, in contrast, be maximal at onset, particularly in embolic infarction.

Symptoms that spontaneously improve or resolve suggest ischemia rather than hemorrhage.

altered sensation

Patients often describe sensory loss and paresthesias as numbness.

headache

Usually of insidious onset and gradually increasing intensity in intracerebral hemorrhage.

More common in hemorrhagic stroke than in ischemic stroke, but the absence of headache does not rule out the diagnosis.[3]

Sudden onset with gradual moderation or "most severe headache of my life" (thunderclap headache) suggests subarachnoid hemorrhage.

weakness

Complete or partial loss of muscle strength in face, arm, and/or leg is among the most common stroke presentations.

As with most stroke signs and symptoms, bilateral involvement is uncommon and may reflect alternative etiology.

sensory loss

Cortical sensory loss usually impairs fine sensory processing abilities such as 2-point discrimination, graphesthesia, or stereognosis.

Thalamic hemorrhages can present with sensory loss and pseudoathetosis.

aphasia

Impairment in any language function (fluency, naming, repetition, comprehension) is a sign of dominant hemispheric stroke.

dysarthria

May accompany facial weakness or cerebellar dysfunction.

ataxia

In the absence of muscle weakness, impaired coordination points to hemorrhage involving the cerebellum or its connections with the rest of the brain.

uncommon

history of hematologic disorder

A bleeding diathesis, especially untreated, may lead to hemorrhage.

vertigo

Typically seen in cerebellar hemorrhage.

nausea/vomiting

May be due to posterior circulation hemorrhage or reflect increased intracranial pressure.

With cerebellar hemorrhage, nausea and vomiting may be the only presenting symptom with an unremarkable neurologic exam except for gait ataxia.

altered level of consciousness/coma

Reduced alertness may accompany large hemispheric hemorrhages or posterior fossa hemorrhages.

Prompts higher level of urgency from diagnostic (rule out hemorrhage) and management (breathing and airway protection) standpoints.

Coma is more common with brain stem hemorrhage.

Conditions mimicking stroke (e.g., seizures) need to be excluded.

confusion

Common, especially in older people with previous strokes or cognitive dysfunction.

Fluent, nonrepetitive (Wernicke) aphasia has to be differentiated from confusion, as aphasia is a specific sign of dominant hemisphere injury.

gaze paresis

Often horizontal and unidirectional.

Risk factors

strong

hypertension

This is the most important risk factor associated with increased incidence of intracerebral hemorrhage (ICH).[13][26]​​​ More strongly associated with risk of deep hemispheric intracerebral than of lobar intracerebral hemorrhage.[13][27][28]​​​

advanced age

Associated with increased incidence of intracerebral hemorrhage.​​​[5]​​[28]​​

male sex

Associated with increased incidence of intracerebral hemorrhage, although the difference lessens with age.[10]

Asian, black, and/or Hispanic ethnicity

Associated with increased incidence of intracerebral hemorrhage.​[11][12]​​​​​​[29] Some, but not all, of this increased risk is accounted for by higher prevalence of hypertension.[30][31]

family history of hemorrhagic stroke

Epidemiologic studies show a significant portion of sporadic intracerebral hemorrhage risk is heritable, and that family history of intracerebral hemorrhage is a risk factor.[27]

hemophilia

Hereditary bleeding disorders, including hemophilia, may be complicated by intracerebral hemorrhage.

cerebral amyloid angiopathy

Sporadic cerebral amyloid angiopathy (CAA), a common age-related cerebral small vessel disease, is an important cause of lobar ICH, particularly in older people.[32] The risk of recurrent ICH in patients with CAA is approximately 7% per year compared to about 1% for ICH associated with arteriolosclerosis.[32][33]​​​​​ Most cases of cerebral amyloid angiopathy (CAA) are nonfamilial. CAA can rarely be caused by autosomal dominant mutations involving the amyloid precursor protein, cystatin-C, or transthyretin genes.[16]

Additional nonmodifiable risk factors for recurrent primary lobar hemorrhage have been identified in people with presumed CAA: number of MRI microbleeds, presence of white matter lesions on CT, and the presence of one or more apolipoprotein E epsilon 2 or epsilon 4 alleles.[14][34][35][36]

sickle cell disease

The incidence rate of hemorrhagic stroke in patients with sickle cell anemia increases with age. Structural vascular abnormalities such as moyamoya arteriopathy and aneurysms are common etiologies for hemorrhage.[37]

autosomal dominant mutations in the COL4A1 gene

Rare autosomal dominant mutations in the COL4A1 gene cause intracerebral hemorrhage, retinal hemorrhages, and porencephaly (cyst or cavity in the cerebral hemispheres).[38]

hereditary hemorrhagic telangiectasia

Caused by mutations in the ACVRL1, ENG, or SMAD4 gene. High prevalence of brain arteriovenous malformations (AVMs), which in turn increases the risk of intracerebral hemorrhage.[18]

autosomal dominant mutations in the KRIT1, CCM2, or PDCD10 genes

May lead to cavernous malformations.

anticoagulation

Aspirin confers a small increased risk, with warfarin conferring a more substantial risk.[39][40]​​​​

Oral anticoagulants are associated with reduced risk compared with warfarin.[41]

Overall, people with atrial fibrillation are at increased risk of hemorrhagic stroke.

illicit sympathomimetic drugs

Drugs such as cocaine and amphetamine, are associated with intracerebral hemorrhage.[42][43]

vascular malformations

These include arteriovenous malformations (AVMs), dural arteriovenous fistulas, and cavernous malformations.[44]

The risk of bleeding depends on the type of malformation, pattern of venous drainage, and history of previous bleeds.

Moyamoya disease

Moyamoya syndrome and Moyamoya disease are associated with parenchymal and intraventricular hemorrhage, predominantly in pediatric patients. The rebleeding rate is approximately 7% per year.[55] Patients with this vasculopathy also have an increased risk for cerebral aneurysms.

pregnancy

The risk of nontraumatic ICH is increased during pregnancy and the postpartum period. One retrospective review showed 6.1 pregnancy-related ICH per 100,000 deliveries and 7.1 pregnancy-related ICH per 100,000 at-risk person-years (compared to 5.0 per 100,000 person-years for nonpregnant women in the same age range).[56] The increased risk of ICH associated with pregnancy is largely attributable to ICH occurring in the postpartum period.[56][57] Peripartum angiopathy, eclampsia, HELLP syndrome, and sinus venous thrombosis can cause ICH in pregnant women.[9] Preexisting risk factors associated with ICH include increasing maternal age, nonwhite race, and chronic hypertension.[57]​​​​

weak

smoking

The association with intracerebral hemorrhage is unclear, with only a few studies documenting risk.[45]

One prospective study and meta-analysis concluded that current smokers are at an increased risk of intracerebral hemorrhage.[46]

nonsteroidal anti-inflammatory drugs (NSAIDs)

As a single group, NSAIDs did not have significant correlation with higher incidence of intracerebral hemorrhage, although among users of specific agents (diclofenac and meloxicam) a significant increased risk was observed.[47]

obstructive sleep apnea

Severe obstructive sleep apnea doubles the risk for incident stroke, especially in young to middle-aged people. Continuous positive airway pressure (CPAP) may reduce stroke risk, but trials have not provided a high level of evidence to support the benefits of CPAP for primary stroke prevention.[48][49]

diabetes mellitus

There is some evidence of a modest association between diabetes and risk of intracerebral hemorrhage, although most people with diabetes will also have other risk factors.[46][50][51]​​​​

heavy alcohol abuse

Associated with an increased risk of hemorrhagic stroke.[52] Light to moderate alcohol consumption may be protective against ischemic stroke but not hemorrhagic stroke.

cerebral vasculitis

Although a relatively infrequent cause of intracerebral or subarachnoid hemorrhage, cerebral vasculitis should be considered in the setting of relevant systemic symptoms, an unexplained progressive neurologic disorder, or in a patient lacking risk factors for hemorrhagic stroke. Diagnosis is achieved after a high level of suspicion with conventional angiography and leptomeningeal biopsy.[53]

thrombocytopenia

Platelet counts less than 20,000/microliter are associated with spontaneous hemorrhagic stroke. Factors such as uremia and alcohol abuse are well known to cause dysfunctional platelet aggregation (thrombocytopathy) and act as the main mechanism for bleeding.

long sleep duration and poor sleep quality

Long sleep duration (≥9 hours/night), long midday napping (>90 minutes), and poor sleep quality are independently and jointly associated with higher risks of incident stroke.[54]

leukemia

Leukemia is associated with parenchymal hemorrhage and cerebral venous thrombosis independently of thrombocytopenia.

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