Given the limitations in current methods of diagnosing myocarditis, it is not surprising that its natural history and associated prognosis are as varied as its clinical presentations. A study looking at the outcomes of patients presenting with acute myocarditis found no connection between clinical variables and prognosis.[111]Fuse K, Kodama M, Okura Y, et al. Predictors of disease course in patients with acute myocarditis. Circulation. 2000 Dec 5;102(23):2829-35.
https://www.ahajournals.org/doi/full/10.1161/01.cir.102.23.2829
http://www.ncbi.nlm.nih.gov/pubmed/11104740?tool=bestpractice.com
Despite this, multiple factors have been linked to a favourable or poorer outcome. A definite association exists between the myocarditis-associated risk factor or specific type of myocarditis and the prognosis of the patient.[5]Caforio AL, Pankuweit S, Arbustini E, et al. Current state of knowledge on aetiology, diagnosis, management, and therapy of myocarditis: a position statement of the European Society of Cardiology working group on myocardial and pericardial diseases. Eur Heart J. 2013 Sep;34(33):2636-48.
https://academic.oup.com/eurheartj/article/34/33/2636/408735
http://www.ncbi.nlm.nih.gov/pubmed/23824828?tool=bestpractice.com
Also, the severity of illness at presentation tends to correlate with long-term outcome.
Endomyocardial biopsy (EMB) DNA PCR persistence of cardiotropic viral genome
The prognosis of patients in whom the EMB DNA polymerase chain reaction analysis is positive for a cardiotropic viral genome has been studied. Those who have persistently positive viral genome analysis on EMB demonstrate worsening left ventricular (LV) ejection fraction and outcome when compared with those who test negative on subsequent EMBs.[112]Kühl U, Pauschinger M, Seeberg B, et al. Viral persistence in the myocardium is associated with progressive cardiac dysfunction. Circulation. 2005 Sep 27;112(13):1965-70.
https://www.ahajournals.org/doi/10.1161/circulationaha.105.548156
http://www.ncbi.nlm.nih.gov/pubmed/16172268?tool=bestpractice.com
Fulminant myocarditis
Patients who present with fulminant myocarditis surprisingly tend to have better outcomes than those who present with a clinically milder acute myocarditis. An 11-year study of patients presenting with myocarditis showed a 93% survival free of heart transplantation in patients with fulminant myocarditis as opposed to 45% in patients who presented with acute myocarditis.[113]McCarthy RE 3rd, Boehmer JP, Hruban RH, et al. Long-term outcome of fulminant myocarditis as compared with acute (nonfulminant) myocarditis. N Engl J Med. 2000 Mar 9;342(10):690-5.
https://www.nejm.org/doi/full/10.1056/NEJM200003093421003
http://www.ncbi.nlm.nih.gov/pubmed/10706898?tool=bestpractice.com
Giant cell myocarditis
Despite modest improvement in mortality with immunosuppressive therapy, patients with giant cell myocarditis have the worst outcomes with a median survival of 5.5 months from the onset of heart failure symptoms.[91]Cooper LT Jr, Berry GJ, Shabetai R; Multicenter Giant Cell Myocarditis Study Group Investigators. Idiopathic giant-cell myocarditis - natural history and treatment. N Engl J Med. 1997 Jun 26;336(26):1860-6.
https://www.nejm.org/doi/full/10.1056/NEJM199706263362603
http://www.ncbi.nlm.nih.gov/pubmed/9197214?tool=bestpractice.com
Presentation mimicking MI
Patients presenting with chest pain and ECG changes similar to those seen in ST-segment elevation myocardial infarction have almost uniform recovery without any residual cardiac dysfunction.[17]Dec GW Jr, Waldman H, Southern J, et al. Viral myocarditis mimicking acute myocardial infarction. J Am Coll Cardiol. 1992 Jul;20(1):85-9.
http://www.ncbi.nlm.nih.gov/pubmed/1607543?tool=bestpractice.com
Histological resolution of myocardial inflammation
Patients with histological resolution of myocardial cellular infiltration on repeat EMB tend to have improvement in cardiac function and a favourable clinical outcome.[114]Dec GW Jr, Fallon JT, Southern JF, et al. Relation between histological findings on early repeat right ventricular biopsy and ventricular function in patients with myocarditis. Br Heart J. 1988 Oct;60(4):332-7.
https://heart.bmj.com/content/heartjnl/60/4/332.full.pdf
http://www.ncbi.nlm.nih.gov/pubmed/3190962?tool=bestpractice.com
Serum immunological markers
Patients with idiopathic cardiomyopathy and elevated levels of serum tumour necrosis factor (TNF)-alpha receptor-1 and fas at presentation have a worse clinical course and are more likely to not recover LV function than those with lower levels.[115]Sheppard R, Bedi M, Kubota T, et al. Myocardial expression of fas and recovery of left ventricular function in patients with recent-onset cardiomyopathy. J Am Coll Cardiol. 2005 Sep 20;46(6):1036-42.
http://www.ncbi.nlm.nih.gov/pubmed/16168288?tool=bestpractice.com
Cardiac MRI findings
A normal cardiac MRI indicates a favourable long-term prognosis, regardless of clinical and other findings. Myocardial oedema without fibrosis is also associated with a positive prognosis.[56]Expert Panel on Cardiac Imaging, Rajiah P, Kirsch J, Bolen MA, et al. ACR Appropriateness Criteria® Nonischemic myocardial disease with clinical manifestations (ischemic cardiomyopathy already excluded). J Am Coll Radiol. 2021 May;18(5S):S83-105.
https://www.jacr.org/article/S1546-1440(21)00115-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/33651982?tool=bestpractice.com
Conversely, a significant amount of early and late gadolinium enhancement correlates with a poor prognosis.[56]Expert Panel on Cardiac Imaging, Rajiah P, Kirsch J, Bolen MA, et al. ACR Appropriateness Criteria® Nonischemic myocardial disease with clinical manifestations (ischemic cardiomyopathy already excluded). J Am Coll Radiol. 2021 May;18(5S):S83-105.
https://www.jacr.org/article/S1546-1440(21)00115-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/33651982?tool=bestpractice.com