The goal of treatment is to:
Management of DISH requires a multidisciplinary approach and may include non-pharmacological interventions (e.g., patient education, self-management, physiotherapy), pharmacological therapies, and surgery.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[4]Mader R, Verlaan JJ, Eshed I, et al. Diffuse idiopathic skeletal hyperostosis (DISH): where we are now and where to go next. RMD Open. 2017;3(1):e000472.
https://rmdopen.bmj.com/content/3/1/rmdopen-2017-000472
http://www.ncbi.nlm.nih.gov/pubmed/28955488?tool=bestpractice.com
[57]Mader R. Current therapeutic options in the management of diffuse idiopathic skeletal hyperostosis. Expert Opin Pharmacother. 2005 Jul;6(8):1313-8.
http://www.ncbi.nlm.nih.gov/pubmed/16013982?tool=bestpractice.com
Therapy must be individualised; different treatments can be combined as required. Management strategies are largely extrapolated from the treatment of osteoarthritis.[4]Mader R, Verlaan JJ, Eshed I, et al. Diffuse idiopathic skeletal hyperostosis (DISH): where we are now and where to go next. RMD Open. 2017;3(1):e000472.
https://rmdopen.bmj.com/content/3/1/rmdopen-2017-000472
http://www.ncbi.nlm.nih.gov/pubmed/28955488?tool=bestpractice.com
Patients with DISH are often frail and have comorbidities; therefore, conservative treatment may be more appropriate.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Surgical management may be required in patients with severe symptomatic cervical DISH or in those experiencing serious complications such as unstable spinal fractures, neurological compromise, or airway obstruction.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Non-pharmacological approaches
Non-pharmacological approaches include patient education (with particular emphasis on joint protection and falls/fracture prevention) and exercise/physiotherapy.
Literature on the use of exercise/physiotherapy in patients with DISH is sparse but may be effective in improving balance, stiffness, range of motion, and muscle strength. One study on the effect of a 24-week exercise programme - consisting of mobility, stretching, and strengthening exercises for the cervical, thoracic, and lumbar spine - reported small improvements in physical measures, which achieved significance only for lumbosacral flexion.[58]Al-Herz A, Snip JP, Clark B, et al. Exercise therapy for patients with diffuse idiopathic skeletal hyperostosis. Clin Rheumatol. 2008 Feb;27(2):207-10.
http://www.ncbi.nlm.nih.gov/pubmed/17885726?tool=bestpractice.com
Orthotic insoles may also be considered as an option to improve posture.
Pain management
Paracetamol and/or a non-steroidal anti-inflammatory drug (NSAID) is recommended for the medical management of pain in axial disease. Topical NSAIDs may be trialled in patients with peripheral joint disease. NSAIDs should be used with caution in older people because of increased susceptibility to adverse effects such as gastrointestinal bleeding and cardiovascular events.[59]McCarberg BH. NSAIDs in the older patient: balancing benefits and harms. Pain Med. 2013 Dec;14 Suppl 1:S43-4.
https://academic.oup.com/painmedicine/article/14/suppl_1/S43/1941495
http://www.ncbi.nlm.nih.gov/pubmed/24373111?tool=bestpractice.com
[60]Davis A, Robson J. The dangers of NSAIDs: look both ways. Br J Gen Pract. 2016 Apr;66(645):172-3.
https://bjgp.org/content/66/645/172
http://www.ncbi.nlm.nih.gov/pubmed/27033477?tool=bestpractice.com
Literature on the use of other analgesics, including opioids, is sparse and no definitive recommendations can be made regarding their use. Intra-articular corticosteroid injections are used in practice in some patients with peripheral joint disease, although there are no robust data to support their use in this setting.
Application of heat may be effective in providing temporary relief of pain symptoms.[57]Mader R. Current therapeutic options in the management of diffuse idiopathic skeletal hyperostosis. Expert Opin Pharmacother. 2005 Jul;6(8):1313-8.
http://www.ncbi.nlm.nih.gov/pubmed/16013982?tool=bestpractice.com
Consider referral to a specialist in pain management if pain symptoms are not adequately controlled by simple analgesia.
Metabolic derangements
DISH may be associated with underlying metabolic conditions that are treatable. Manage metabolic derangements, such as obesity, hypertriglyceridaemia, low high-density lipoprotein cholesterol level, hypertension, hyperuricaemia, and hyperglycaemia.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[57]Mader R. Current therapeutic options in the management of diffuse idiopathic skeletal hyperostosis. Expert Opin Pharmacother. 2005 Jul;6(8):1313-8.
http://www.ncbi.nlm.nih.gov/pubmed/16013982?tool=bestpractice.com
See Metabolic syndrome, Hypertriglyceridaemia, Hypercholesterolaemia, Essential hypertension, Gout, and Type 2 diabetes in adults.
Dysphagia and airway impairment
Exuberant bone formation over the cervical spine anterior to the vertebral bodies can cause the oesophagus or trachea to be displaced, potentially leading to dysphagia or airway obstruction. This may subsequently contribute to the development of obstructive sleep apnoea and post-obstructive pneumonia.[2]Kuperus JS, Mohamed Hoesein FAA, de Jong PA, et al. Diffuse idiopathic skeletal hyperostosis: etiology and clinical relevance. Best Pract Res Clin Rheumatol. 2020 Jun;34(3):101527.
https://www.sciencedirect.com/science/article/pii/S1521694220300449
http://www.ncbi.nlm.nih.gov/pubmed/32456997?tool=bestpractice.com
For patients with dysphagia or airway issues, always involve an otolaryngologist and/or speech therapist.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
If the dysphagia is mild, manage conservatively with dietary changes (modifying texture to soft, pureed foods), swallowing therapy, and medical management.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
If there is airway impairment and/or severe dysphagia, obtain urgent orthopaedic input for consideration of surgical osteophyte removal.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[61]Castellano DM, Sinacori JT, Karakla DW. Stridor and dysphagia in diffuse idiopathic skeletal hyperostosis (DISH). Laryngoscope. 2006 Feb;116(2):341-4.
http://www.ncbi.nlm.nih.gov/pubmed/16467731?tool=bestpractice.com
For surgical resection of anterior cervical osteophytes, trans-oral, posterolateral, and anterior cervical osteophyte exposures have been used. However, the left anterolateral technique is frequently employed because it is convenient for spinal surgeons and may reduce the risk of injury to the recurrent laryngeal nerve.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
The anterolateral approach is particularly preferred given the ease of osteophyte removal and extended approach from C2-T1.[62]Harlianto NI, Kuperus JS, Verlaan JJ. Perioperative management, operative techniques, and pitfalls in the surgical treatment of patients with diffuse idiopathic skeletal hyperostosis: a narrative review. Explor Musculoskeletal Dis. 2023;1:84-96.
https://www.explorationpub.com/Journals/emd/Article/100713
Risks associated with surgery are usually related to patient frailty or distorted anatomy.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Neurological symptoms
As a consequence of the ankylosed spine and subsequent impingement on the spinal canal, patients with DISH have a higher likelihood of neurological deficit, particularly after trauma.[62]Harlianto NI, Kuperus JS, Verlaan JJ. Perioperative management, operative techniques, and pitfalls in the surgical treatment of patients with diffuse idiopathic skeletal hyperostosis: a narrative review. Explor Musculoskeletal Dis. 2023;1:84-96.
https://www.explorationpub.com/Journals/emd/Article/100713
Seek specialist input for consideration of surgical decompression for progressive neurological symptoms, such as with spinal stenosis, myelopathy, or radiculopathy.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Robust literature on the management of neurological symptoms in patients with DISH is lacking.
Fractures
Patients with DISH are at increased risk of vertebral body fractures. DISH increases the risk of unstable spine fractures, which can result from low-energy mechanisms such as ground-level falls, tenfold.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[63]Reinhold M, Knop C, Kneitz C, et al. Spine fractures in ankylosing diseases: recommendations of the spine section of the German Society for Orthopaedics and Trauma (DGOU). Global Spine J. 2018 Sep;8(2 suppl):56-68S.
https://journals.sagepub.com/doi/10.1177/2192568217736268
http://www.ncbi.nlm.nih.gov/pubmed/30210963?tool=bestpractice.com
The most frequent fractures seen in individuals with DISH are hyperextension fractures through fused vertebral bodies. The most commonly affected segments of the spine are the cervical, thoracic, and lumbar, in that order.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Seek orthopaedic assessment for patients with a fracture associated with DISH as these patients are usually managed with surgery. Non-surgical management is typically reserved for individuals without neurological compromise who have medical conditions that make surgery unsuitable, because immobilisation with an orthosis alone is linked to problems such as fracture displacement with consequent neurological dysfunction and increasing deformity.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[63]Reinhold M, Knop C, Kneitz C, et al. Spine fractures in ankylosing diseases: recommendations of the spine section of the German Society for Orthopaedics and Trauma (DGOU). Global Spine J. 2018 Sep;8(2 suppl):56-68S.
https://journals.sagepub.com/doi/10.1177/2192568217736268
http://www.ncbi.nlm.nih.gov/pubmed/30210963?tool=bestpractice.com
Patients with DISH frequently have fixed kyphotic deformities, making the bracing treatment of thoracolumbar fractures challenging.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Compared with non-surgical treatment of fractures, surgical management is linked to lower mortality rates.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
If surgery is indicated, important factors to consider when choosing a technique include the patient's comorbidities, the presence of neurological deficits, any pre-existing deformities, and the requirement for fracture reduction.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Surgical techniques typically used in patients suitable for surgery are open pedicle screw fixation and percutaneous pedicle screw (if no neurological deficit is present).
Studies show that, compared with open fixation, percutaneous stabilisation results in reduced blood loss, shorter operating times, fewer transfusion requirements, and lower perioperative complication rates.[62]Harlianto NI, Kuperus JS, Verlaan JJ. Perioperative management, operative techniques, and pitfalls in the surgical treatment of patients with diffuse idiopathic skeletal hyperostosis: a narrative review. Explor Musculoskeletal Dis. 2023;1:84-96.
https://www.explorationpub.com/Journals/emd/Article/100713
Corrective osteotomies are rarely advised as part of the surgical management of spinal fractures, even in the presence of significant baseline kyphotic abnormalities.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
These procedures may increase spinal instability or increase the likelihood of pseudoarthrosis and implant failure.[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
Management options in patients without neurological compromise who are unsuitable for surgical intervention include:[1]Le HV, Wick JB, Van BW, et al. Diffuse idiopathic skeletal hyperostosis of the spine: pathophysiology, diagnosis, and management. J Am Acad Orthop Surg. 2021 Dec 15;29(24):1044-51.
http://www.ncbi.nlm.nih.gov/pubmed/34559699?tool=bestpractice.com
[64]Taher AW, Page PS, Greeneway GP, et al. Spinal fractures in the setting of diffuse idiopathic skeletal hyperostosis conservatively treated via orthosis: illustrative cases. J Neurosurg Case Lessons. 2022 May 16;3(20):CASE21689.
https://thejns.org/caselessons/view/journals/j-neurosurg-case-lessons/3/20/article-CASE21689.xml
http://www.ncbi.nlm.nih.gov/pubmed/36303482?tool=bestpractice.com
Serial neurological examination is recommended in those who are unsuitable for surgical intervention to assess for development of neurological deficit.
Analgesia for patients with fractures should begin with non-opioid drugs such as paracetamol and NSAIDs. Data from animal studies on the impairment of fracture healing by NSAIDs are inconclusive, and these agents are regularly used clinically for this indication.[65]Borgeat A, Ofner C, Saporito A, et al. The effect of nonsteroidal anti-inflammatory drugs on bone healing in humans: a qualitative, systematic review. J Clin Anesth. 2018 Sep;49:92-100.
http://www.ncbi.nlm.nih.gov/pubmed/29913395?tool=bestpractice.com
[66]Marquez-Lara A, Hutchinson ID, Nuñez F Jr, et al. Nonsteroidal anti-inflammatory drugs and bone-healing: a systematic review of research quality. JBJS Rev. 2016 Mar 15;4(3):e4.
https://journals.lww.com/jbjsreviews/fulltext/2016/03000/nonsteroidal_anti_inflammatory_drugs_and.4.aspx
http://www.ncbi.nlm.nih.gov/pubmed/27500434?tool=bestpractice.com
If stronger analgesia is required, opioids can be used in combination with paracetamol. If opioids are used, a laxative should also be prescribed and fluid intake encouraged to prevent constipation. If used chronically, opioids may lose potency, induce dependence, raise risk for addiction, and lead to falls and central sensitisation.[67]LeBoff MS, Greenspan SL, Insogna KL, et al. The clinician's guide to prevention and treatment of osteoporosis. Osteoporos Int. 2022 Oct;33(10):2049-102.
https://link.springer.com/article/10.1007/s00198-021-05900-y
http://www.ncbi.nlm.nih.gov/pubmed/35478046?tool=bestpractice.com
Opioids are recommended only for very short-term use with acute fractures.
For persistent severe pain, use of centrally-acting therapies including tricyclic antidepressants and gabapentin should be considered after discussion about the potential risks and benefits.
A period of immobilisation or rest is recommended post fracture while the patient continues to be in acute pain. Physiotherapy and exercise programmes can be initiated when the degree of pain starts to diminish; prolonged immobilisation is not recommended.