In-hospital mortality and predictors
Overall mortality associated with status epilepticus approaches 20% and does not appear to be changing with time.[6]Dham BS, Hunter K, Rincon F. The epidemiology of status epilepticus in the United States. Neurocrit Care. 2014 Jun;20(3):476-83.
http://www.ncbi.nlm.nih.gov/pubmed/24519080?tool=bestpractice.com
[7]DeLorenzo RJ, Hauser WA, Towne AR, et al. A prospective, population-based epidemiologic study of status epilepticus in Richmond, Virginia. Neurology. 1996 Apr;46(4):1029-35.
http://www.ncbi.nlm.nih.gov/pubmed/8780085?tool=bestpractice.com
[63]Hesdorffer DC, Logroscino G, Cascino G, et al. Incidence of status epilepticus in Rochester, Minnesota, 1965-1984. Neurology. 1998 Mar;50(3):735-41.
http://www.ncbi.nlm.nih.gov/pubmed/9521266?tool=bestpractice.com
[64]Betjemann JP, Lowenstein DH. Status epilepticus in adults. Lancet Neurol. 2015 Jun;14(6):615-24.
http://www.ncbi.nlm.nih.gov/pubmed/25908090?tool=bestpractice.com
One study of patients with generalised convulsive status epilepticus of all ages reported an in-hospital mortality rate of 3.45%.[65]Koubeissi M, Alshekhlee A. In-hospital mortality of generalized convulsive status epilepticus: a large US sample. Neurology. 2007 Aug 28;69(9):886-93.
http://www.ncbi.nlm.nih.gov/pubmed/17724291?tool=bestpractice.com
Predictors of mortality included older age, higher comorbidity index, use of mechanical ventilation, and hypoxic brain injury. Despite changes in management, epidemiological studies have not shown a marked change in status epilepticus-related mortality rates in high-income countries over the past decades, although reported rates are variable across studies.[64]Betjemann JP, Lowenstein DH. Status epilepticus in adults. Lancet Neurol. 2015 Jun;14(6):615-24.
http://www.ncbi.nlm.nih.gov/pubmed/25908090?tool=bestpractice.com
Numerous other studies have found acute symptomatic aetiology (such as cerebrovascular accidents or post-anoxic injuries) and longer duration of status epilepticus to predict a poorer prognosis.[64]Betjemann JP, Lowenstein DH. Status epilepticus in adults. Lancet Neurol. 2015 Jun;14(6):615-24.
http://www.ncbi.nlm.nih.gov/pubmed/25908090?tool=bestpractice.com
[66]Shorvon S, Sen A. What is status epilepticus and what do we know about its epidemiology? Seizure. 2020 Feb;75:131-6.
https://www.seizure-journal.com/article/S1059-1311(19)30215-8/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/31786006?tool=bestpractice.com
Alcohol-related or poor-compliance-related status epilepticus carries a more favourable outcome than status epilepticus of other causes, but recovery of these patients is usually marked by a prolonged post-ictal state.[8]Hauser WA. Status epilepticus: epidemiologic considerations. Neurology. 1990 May;40(5 suppl 2):S9-S13.
http://www.ncbi.nlm.nih.gov/pubmed/2185441?tool=bestpractice.com
[67]Neligan A, Shorvon SD. Frequency and prognosis of convulsive status epilepticus of different causes: a systematic review. Arch Neurol. 2010 Aug;67(8):931-40.
http://www.ncbi.nlm.nih.gov/pubmed/20697043?tool=bestpractice.com
Super-refractory status epilepticus (SRSE) is defined as status epilepticus that continues or recurs 24 hours or more after the onset of anaesthetic therapy or recurs on the reduction/withdrawal of anaesthesia.[68]Shorvon S, Ferlisi M. The treatment of super-refractory status epilepticus: a critical review of available therapies and a clinical treatment protocol. Brain. 2011 Oct;134(pt 10):2802-18.
http://www.ncbi.nlm.nih.gov/pubmed/21914716?tool=bestpractice.com
[69]Cornwall CD, Krøigård T, Kristensen JSS, et al. Outcomes and treatment approaches for super-refractory status epilepticus: a systematic review and meta-analysis. JAMA Neurol. 2023 Jul 31;80(9):959-68.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10391362
http://www.ncbi.nlm.nih.gov/pubmed/37523161?tool=bestpractice.com
One systematic review and meta-analysis showed the outcome of SRSE is poor with a reported in-hospital mortality of 24.1%.[69]Cornwall CD, Krøigård T, Kristensen JSS, et al. Outcomes and treatment approaches for super-refractory status epilepticus: a systematic review and meta-analysis. JAMA Neurol. 2023 Jul 31;80(9):959-68.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10391362
http://www.ncbi.nlm.nih.gov/pubmed/37523161?tool=bestpractice.com
Only around one-quarter of patients had an modified Rankin Scale (mRS) of 2 or less (2=slight disability, unable to perform all previous activities but able to look after own affairs without assistance; 1=no significant disability despite symptoms, able to carry out all usual duties and activities; 0=no symptoms) and less than 10% were completely independent at discharge.[69]Cornwall CD, Krøigård T, Kristensen JSS, et al. Outcomes and treatment approaches for super-refractory status epilepticus: a systematic review and meta-analysis. JAMA Neurol. 2023 Jul 31;80(9):959-68.
https://pmc.ncbi.nlm.nih.gov/articles/PMC10391362
http://www.ncbi.nlm.nih.gov/pubmed/37523161?tool=bestpractice.com
Long-term follow-up
Long-term outcomes of status epilepticus vary significantly according to the underlying aetiology, duration of seizures, age, sex, medical comorbidities, incidence of in-hospital complications, and treatment location.[70]Migdady I, Rosenthal ES, Cock HR. Management of status epilepticus: a narrative review. Anaesthesia. 2022 Jan;77 suppl 1:78-91.
http://www.ncbi.nlm.nih.gov/pubmed/35001380?tool=bestpractice.com
One study reported that 7 of 8 survivors of refractory status epilepticus (treated with a standardised protocol of pentobarbital coma) remained stable for a mean 2.9 years following hospital discharge.[71]Yaffe K, Lowenstein DH. Prognostic factors of pentobarbital therapy for refractory generalized status epilepticus. Neurology. 1993 May;43(5):895-900.
http://www.ncbi.nlm.nih.gov/pubmed/8492944?tool=bestpractice.com
A subsequent report noted a 1-year recurrence rate of 17% for paediatric status epilepticus.[72]Neville BG, Chin RF, Scott RC. Childhood convulsive status epilepticus: epidemiology, management and outcome. Acta Neurol Scand Suppl. 2007;186:21-4.
http://www.ncbi.nlm.nih.gov/pubmed/17784533?tool=bestpractice.com
Patients recovering from status epilepticus often continue to have neurological deficits, especially in memory and other cognitive areas.[70]Migdady I, Rosenthal ES, Cock HR. Management of status epilepticus: a narrative review. Anaesthesia. 2022 Jan;77 suppl 1:78-91.
http://www.ncbi.nlm.nih.gov/pubmed/35001380?tool=bestpractice.com
This is likely to be secondary to excitotoxic injury of one or both hippocampi.[73]Jambaque I, Hertz-Pannier L, Mikaeloff Y, et al. Severe memory impairment in a child with bihippocampal injury after status epilepticus. Dev Med Child Neurol. 2006 Mar;48(3):223-6.
http://onlinelibrary.wiley.com/doi/10.1017/S0012162206000478/pdf
http://www.ncbi.nlm.nih.gov/pubmed/16483400?tool=bestpractice.com