Etiology

Based on the etiology, hirsutism can be divided into 3 categories: idiopathic, hyperandrogenic, and nonandrogenic.[2]

Idiopathic hirsutism

These women have no identifiable etiology for the excessive hair growth. They have normal androgen levels and regular menstrual cycles. Idiopathic hirsutism accounts for 5% to 15% of all cases. Possible causes include increased androgenic sensitivity in the pilosebaceous unit, increase in conversion of testosterone to dihydrotestosterone, or androgen receptors changing their function.[2]

Hyperandrogenic hirsutism

Hyperandrogenic hirsutism (HH) is the most common category, responsible for over 80% of cases and is usually caused by an overproduction of androgen from the ovaries or adrenal glands. Patients with HH typically have irregular menses, anovulation, infertility, hyperinsulinemia, and have a greater risk of developing endometrial hyperplasia or neoplasia due to the unopposed estrogen.[2] Causes of HH include:

  • Polycystic ovary syndrome (PCOS): accounts for 72% to 82% of all hirsutism cases

  • Nonclassic congenital adrenal hyperplasia

  • Androgen-secreting ovarian tumors

    • Sertoli-Leydig cell tumors (androblastoma, arrhenoblastoma)

    • Granulosa-theca cell tumors

    • Hilus-cell tumors

  • Ovarian hyperthecosis (a condition with features similar to PCOS, but with more severe androgenization). May occur postmenopausally; the cause is luteinized theca cells, which become hormonally active.

Nonandrogenic hirsutism

Women may develop hirsutism due to certain drugs, such as:[2]

  • Danazol

  • Performance-enhancing anabolic steroids

  • Cyclosporine

  • Diazoxide

  • Penicillamine

  • Interferon

  • Phenytoin

  • Cetuximab

  • Corticosteroids

  • Androgen creams or patches

  • Progestins

  • Estrogen antagonists (e.g., tamoxifen).

Endocrinopathies, such as hypo- or hyperthyroidism, hyperprolactinemia, or Cushing syndrome may also cause hirsutism, though this is uncommon and usually associated with other signs and symptoms of these conditions.

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