Epidemiology

Pancreatic neuroendocrine tumours account for <2% of all cancers arising in the pancreas.[6]

Epidemiological data for specific types of neuroendocrine tumours are scant. In the US, the incidence rate of pancreatic neuroendocrine tumours has risen from 0.27 to 1.00 per 100,000 persons from 2000 to 2016 (based on Surveillance, Epidemiology, and End Results [SEER] data). This increase has been attributed to improved diagnostic techniques and increased detection of localised disease.[7]

Modest data suggest that men and women are equally affected by neuroendocrine tumours, including VIPoma.[8][9]​ Median age at diagnosis of 51 years (range 11-75 years) has been derived from individual case reports.[9]

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