The diagnosis of HRS is based on clinical criteria.[2]Biggins SW, Angeli P, Garcia-Tsao G, et al. Diagnosis, evaluation, and management of ascites, spontaneous bacterial peritonitis and hepatorenal syndrome: 2021 practice guidance by the American Association for the Study of Liver Diseases. Hepatology. 2021 Aug;74(2):1014-48.
https://aasldpubs.onlinelibrary.wiley.com/doi/10.1002/hep.31884
http://www.ncbi.nlm.nih.gov/pubmed/33942342?tool=bestpractice.com
[4]Angeli P, Ginès P, Wong F, et al. Diagnosis and management of acute kidney injury in patients with cirrhosis: revised consensus recommendations of the International Club of Ascites. J Hepatol. 2015 Apr;62(4):968-74.
https://www.journal-of-hepatology.eu/article/S0168-8278(14)00958-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/25638527?tool=bestpractice.com
[5]Simonetto DA, Gines P, Kamath PS. Hepatorenal syndrome: pathophysiology, diagnosis, and management. BMJ. 2020 Sep 14;370:m2687.
http://diposit.ub.edu/dspace/bitstream/2445/175684/1/705291.pdf
http://www.ncbi.nlm.nih.gov/pubmed/32928750?tool=bestpractice.com
[8]European Association for the Study of the Liver. EASL clinical practice guidelines for the management of patients with decompensated cirrhosis. J Hepatol. 2018 Aug;69(2):406-60.
https://www.journal-of-hepatology.eu/article/S0168-8278(18)31966-4/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/29653741?tool=bestpractice.com
[18]Salerno F, Gerbes A, Gines P, et al. Diagnosis, prevention and treatment of hepatorenal syndrome in cirrhosis. Gut. 2007 Sep;56(9):1310-8.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1954971
http://www.ncbi.nlm.nih.gov/pubmed/17389705?tool=bestpractice.com
(See Classification and Diagnostic Criteria sections.)
HRS may develop in any patient with advanced liver disease and presence of portal hypertension-related ascites.[17]Angeli P, Merkel C. Pathogenesis and management of hepatorenal syndrome in patients with cirrhosis. J Hepatol. 2008;48 Suppl 1:S93-103.
https://www.journal-of-hepatology.eu/article/S0168-8278(08)00056-1/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/18304678?tool=bestpractice.com
Patients rarely present with oliguria or symptoms of uraemia. The most common cause of type 1 HRS in Europe is alcoholic hepatitis.
History and physical examination
Other causes of renal failure need to be excluded.[18]Salerno F, Gerbes A, Gines P, et al. Diagnosis, prevention and treatment of hepatorenal syndrome in cirrhosis. Gut. 2007 Sep;56(9):1310-8.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1954971
http://www.ncbi.nlm.nih.gov/pubmed/17389705?tool=bestpractice.com
The patient should be asked about their current medicine use and whether there has been any recent change, such as an increase in diuretic dosage or use of non-steroidal anti-inflammatory drugs. A history of repeated vomiting or diarrhoea, or gastrointestinal bleeding (e.g., haematemesis or melaena stools) suggests volume depletion. Fever, a productive cough, dysuria, and abdominal pain may indicate the presence of infection.
Examination may show the signs of chronic liver disease, such as spider angioma, bruising, petechiae, palmar erythema, jaundice, and scratch marks. Encephalopathy with confusion, decreased level of consciousness, and asterixis may be present. Gynaecomastia may be present in men. Most patients have at least modest lowering of blood pressure.
Abdominal examination may reveal ascites, and the patient may also have splenomegaly. Abdominal tenderness may be suggestive of spontaneous bacterial peritonitis.
Tests
Blood should be sent for full blood count, electrolytes, renal function (creatinine and urea), liver tests, and coagulation profile.
To diagnose HRS-AKI, it is important to exclude structural kidney injury, which relies on history but may be supported by urine microscopy findings. Due to significant overlap between HRS, pre-renal renal failure, and acute tubular necrosis, urine sodium as well as fractional excretion of sodium are not part of the diagnostic criteria of HRS-AKI.[5]Simonetto DA, Gines P, Kamath PS. Hepatorenal syndrome: pathophysiology, diagnosis, and management. BMJ. 2020 Sep 14;370:m2687.
http://diposit.ub.edu/dspace/bitstream/2445/175684/1/705291.pdf
http://www.ncbi.nlm.nih.gov/pubmed/32928750?tool=bestpractice.com
A septic work-up consisting of blood, urine, and ascitic fluid culture, urinalysis, and chest x-ray must be performed to exclude sepsis.
Renal ultrasound also must be performed to exclude an obstructive cause of renal failure.