Mortality in melioidosis without specific antibiotic therapy can be >50% overall and >90% in septic shock cases. Even with appropriate antibiotics, delayed diagnosis and lack of access to state-of-the-art intensive care therapy is currently associated with overall mortality rates of around 40% in many endemic locations.[65]Stephens DP, Thomas JH, Ward LM, et al. Melioidosis causing critical illness: a review of 24 years experience from the Royal Darwin Hospital ICU. Crit Care Med. 2016;44:1500-1505.
http://www.ncbi.nlm.nih.gov/pubmed/26963328?tool=bestpractice.com
The priority in melioidosis-endemic regions is to have adequate laboratory microbiology (most critically blood culture capability) to enable timely diagnosis by culture and identification of Burkholderia pseudomallei. Once a diagnosis is made, the antibiotic therapy is divided into the intensive intravenous phase, followed by the oral eradication phase. The therapy of glanders in humans follows the same recommendations as for melioidosis.
Healthcare workers caring for infected patients should use standard contact precautions. The US Centers for Disease Control and Prevention (CDC) recommends the use of standard and airborne precautions when treating patients with glanders.[83]Centers for Disease Control and Prevention. Glanders: healthcare response activities. Oct 2017 [internet publication].
https://www.cdc.gov/glanders/bioterrorism-response-planning/healthcare-response-activities.html
In some endemic areas, melioidosis and glanders are statutorily notifiable diseases which must be reported to local health authorities. In non-endemic areas this is now also a common requirement in the light of their potential use as biothreat agents; in the US bothBurkholderia mallei and B pseudomallei are categorised as Tier 1 select agents.[5]Federal Select Agent Program. Select agents and toxins list. 2017 [internet publication].
http://www.selectagents.gov/SelectAgentsandToxinsList.html
Intensive intravenous antibiotic therapy
Intravenous antibiotic therapy with ceftazidime, meropenem, or imipenem/cilastatin should be administered in non-localised disease or patients who are systemically unwell.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[43]Wiersinga WJ, Currie BJ, Peacock SJ. Melioidosis. N Engl J Med. 2012;367:1035-1044.
http://www.ncbi.nlm.nih.gov/pubmed/22970946?tool=bestpractice.com
[84]Pitman MC, Luck T, Marshall CS, et al. Intravenous therapy duration and outcomes in melioidosis: a new treatment paradigm. PloS Negl Trop Dis. 2015;9:e0003586.
http://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0003586
http://www.ncbi.nlm.nih.gov/pubmed/25811783?tool=bestpractice.com
[57]Lipsitz R, Garges S, Aurigemma R, et al. Workshop on treatment of and postexposure prophylaxis for Burkholderia pseudomallei and B. mallei infection, 2010. Emerg Infect Dis. 2012;18:e2.
http://wwwnc.cdc.gov/eid/article/18/12/12-0638_article
http://www.ncbi.nlm.nih.gov/pubmed/23171644?tool=bestpractice.com
[85]Dance D. Treatment and prophylaxis of melioidosis. Int J Antimicrob Agents. 2014;43:310-318.
http://www.sciencedirect.com/science/article/pii/S0924857914000181
http://www.ncbi.nlm.nih.gov/pubmed/24613038?tool=bestpractice.com
In patients with a collection (including skin ulcers/abscesses and abscesses in internal organs), and in bone/joint, genitourinary, and CNS infections (but not for pneumonia), intravenous (if available) or oral trimethoprim/sulfamethoxazole may be added.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[86]Chierakul W, Anunnatsiri S, Short JM, et al. Two randomized controlled trials of ceftazidime alone versus ceftazidime in combination with trimethoprim-sulfamethoxazole for the treatment of severe melioidosis. Clin Infect Dis. 2005;41:1105-1113.
http://cid.oxfordjournals.org/content/41/8/1105.long
http://www.ncbi.nlm.nih.gov/pubmed/16163628?tool=bestpractice.com
Concomitant administration of folic acid should be considered when giving trimethoprim/sulfamethoxazole in high doses for a long duration to reduce potential adverse effects associated with the drug’s anti-folate effect (e.g., bone marrow toxicity).[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
Duration of therapy is determined by the severity and nature of the clinical features.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[84]Pitman MC, Luck T, Marshall CS, et al. Intravenous therapy duration and outcomes in melioidosis: a new treatment paradigm. PloS Negl Trop Dis. 2015;9:e0003586.
http://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0003586
http://www.ncbi.nlm.nih.gov/pubmed/25811783?tool=bestpractice.com
Minimum duration is 10 to 14 days, which should be extended to 4 weeks if:
Pneumonia requiring ICU or associated with mediastinal lymphadenopathy or extensive bilateral chest x-ray changes
Presence of internal organ abscesses, septic arthritis, or other deep-seated collections, with 4-week duration timed from last aspiration of pus (e.g., with prostatic abscesses or septic arthritis).
Duration should be extended to 6 weeks (minimum) if osteomyelitis is present.
Duration should be extended to 8 weeks if the patient has neurological melioidosis or mycotic aneurysm.
In resource-poor settings it may not be affordable to extend treatment, but a minimum of 10 to 14 days of intensive treatment is recommended.[57]Lipsitz R, Garges S, Aurigemma R, et al. Workshop on treatment of and postexposure prophylaxis for Burkholderia pseudomallei and B. mallei infection, 2010. Emerg Infect Dis. 2012;18:e2.
http://wwwnc.cdc.gov/eid/article/18/12/12-0638_article
http://www.ncbi.nlm.nih.gov/pubmed/23171644?tool=bestpractice.com
[87]Dance DA, Davong V, Soeng S, et al. Trimethoprim/sulfamethoxazole resistance in Burkholderia pseudomallei. Int J Antimicrob Agents. 2014;44:368-369.
http://www.sciencedirect.com/science/article/pii/S0924857914001976
http://www.ncbi.nlm.nih.gov/pubmed/25245211?tool=bestpractice.com
In this situation the importance of completing a full course of oral eradication therapy is paramount.
Oral eradication therapy
Oral trimethoprim/sulfamethoxazole is the treatment of choice after intensive intravenous antibiotic therapy, or in patients with localised disease who are systemically well.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[43]Wiersinga WJ, Currie BJ, Peacock SJ. Melioidosis. N Engl J Med. 2012;367:1035-1044.
http://www.ncbi.nlm.nih.gov/pubmed/22970946?tool=bestpractice.com
[84]Pitman MC, Luck T, Marshall CS, et al. Intravenous therapy duration and outcomes in melioidosis: a new treatment paradigm. PloS Negl Trop Dis. 2015;9:e0003586.
http://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0003586
http://www.ncbi.nlm.nih.gov/pubmed/25811783?tool=bestpractice.com
[57]Lipsitz R, Garges S, Aurigemma R, et al. Workshop on treatment of and postexposure prophylaxis for Burkholderia pseudomallei and B. mallei infection, 2010. Emerg Infect Dis. 2012;18:e2.
http://wwwnc.cdc.gov/eid/article/18/12/12-0638_article
http://www.ncbi.nlm.nih.gov/pubmed/23171644?tool=bestpractice.com
[85]Dance D. Treatment and prophylaxis of melioidosis. Int J Antimicrob Agents. 2014;43:310-318.
http://www.sciencedirect.com/science/article/pii/S0924857914000181
http://www.ncbi.nlm.nih.gov/pubmed/24613038?tool=bestpractice.com
[88]Chetchotisakd P, Chierakul W, Chaowagul W, et al. Trimethoprim-sulfamethoxazole versus trimethoprim-sulfamethoxazole plus doxycycline as oral eradicative treatment for melioidosis (MERTH): a multicentre, double-blind, non-inferiority, randomised controlled trial. Lancet. 2014;383:807-814.
http://www.sciencedirect.com/science/article/pii/S0140673613619510
http://www.ncbi.nlm.nih.gov/pubmed/24284287?tool=bestpractice.com
[89]Cheng AC, McBryde ES, Wuthiekanun V, et al. Dosing regimens of cotrimoxazole (trimethoprim-sulfamethoxazole) for melioidosis. Antimicrob Agents Chemother. 2009;53:4193-4199.
http://aac.asm.org/content/53/10/4193.long
http://www.ncbi.nlm.nih.gov/pubmed/19620336?tool=bestpractice.com
Concomitant administration of folic acid should be considered when giving trimethoprim/sulfamethoxazole in high doses for a long duration to reduce potential adverse effects associated with the drug’s anti-folate effect (e.g., bone marrow toxicity).[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
However, bone marrow suppression, rash, and hyperkalaemia and elevated creatinine are not uncommonly seen in melioidosis patients treated with trimethoprim/sulfamethoxazole. One study found that 30% of patients treated with trimethoprim/sulfamethoxazole experienced adverse effects which required cessation, a reduction in dose, or change in antibiotic.[90]Sullivan RP, Ward L, Currie BJ. Oral eradication therapy for melioidosis: Important but not without risks. Int J Infect Dis. 2019 Mar;80:111-114.
https://www.doi.org/10.1016/j.ijid.2019.01.019
http://www.ncbi.nlm.nih.gov/pubmed/30659921?tool=bestpractice.com
Alternative eradication therapy for these patients is amoxicillin/clavulanate, or doxycycline (in adults only).[91]Cheng AC, Chierakul W, Chaowagul W, et al. Consensus guidelines for dosing of amoxicillin-clavulanate in melioidosis. Am J Trop Med Hyg. 2008;78:208-209.
http://www.ajtmh.org/content/78/2/208.long
http://www.ncbi.nlm.nih.gov/pubmed/18256414?tool=bestpractice.com
In children older than 2 months of age and pregnant women, trimethoprim/sulfamethoxazole remains the drug of choice, although delaying the use of trimethoprim/sulfamethoxazole until beyond the first trimester can be considered because of concerns of teratogenicity. Amoxicillin/clavulanate is an alternative, although it has been associated with a relatively high risk of recurrence.[85]Dance D. Treatment and prophylaxis of melioidosis. Int J Antimicrob Agents. 2014;43:310-318.
http://www.sciencedirect.com/science/article/pii/S0924857914000181
http://www.ncbi.nlm.nih.gov/pubmed/24613038?tool=bestpractice.com
Eradication therapy should be continued for a minimum of 3 months, and extended to 6 months if neurological melioidosis or osteomyelitis are present.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[43]Wiersinga WJ, Currie BJ, Peacock SJ. Melioidosis. N Engl J Med. 2012;367:1035-1044.
http://www.ncbi.nlm.nih.gov/pubmed/22970946?tool=bestpractice.com
[84]Pitman MC, Luck T, Marshall CS, et al. Intravenous therapy duration and outcomes in melioidosis: a new treatment paradigm. PloS Negl Trop Dis. 2015;9:e0003586.
http://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0003586
http://www.ncbi.nlm.nih.gov/pubmed/25811783?tool=bestpractice.com
[85]Dance D. Treatment and prophylaxis of melioidosis. Int J Antimicrob Agents. 2014;43:310-318.
http://www.sciencedirect.com/science/article/pii/S0924857914000181
http://www.ncbi.nlm.nih.gov/pubmed/24613038?tool=bestpractice.com
Some patients with localised disease (confirmed by imaging to exclude other foci) who are systemically well may safely be treated with oral eradication therapy alone.[10]McLeod C, Morris PS, Bauert PA, et al. Clinical presentation and medical management of melioidosis in children: a 24-year prospective study in the Northern Territory of Australia and review of the literature. Clin Infect Dis. 2015;60:21-26.
http://cid.oxfordjournals.org/content/60/1/21.long
http://www.ncbi.nlm.nih.gov/pubmed/25228703?tool=bestpractice.com
[85]Dance D. Treatment and prophylaxis of melioidosis. Int J Antimicrob Agents. 2014;43:310-318.
http://www.sciencedirect.com/science/article/pii/S0924857914000181
http://www.ncbi.nlm.nih.gov/pubmed/24613038?tool=bestpractice.com
Treatment of abscesses
Collections should be drained where practicable (especially prostate and muscle abscesses and larger liver abscesses), but splenic abscesses usually do not require drainage.
Duration of intravenous therapy is best timed from last culture-positive drainage of pus.[84]Pitman MC, Luck T, Marshall CS, et al. Intravenous therapy duration and outcomes in melioidosis: a new treatment paradigm. PloS Negl Trop Dis. 2015;9:e0003586.
http://journals.plos.org/plosntds/article?id=10.1371/journal.pntd.0003586
http://www.ncbi.nlm.nih.gov/pubmed/25811783?tool=bestpractice.com
Melioidosis septic shock
State-of-the-art resuscitation and intensive care therapy with severe sepsis guidelines are necessary to reach the current best-care overall mortality of 10%.[65]Stephens DP, Thomas JH, Ward LM, et al. Melioidosis causing critical illness: a review of 24 years experience from the Royal Darwin Hospital ICU. Crit Care Med. 2016;44:1500-1505.
http://www.ncbi.nlm.nih.gov/pubmed/26963328?tool=bestpractice.com
The mortality benefit of adding granulocyte-colony stimulating factor (G-CSF) to the treatment regimen in patients with melioidosis septic shock remains unproven, but it is used in some intensive care units experienced in treating melioidosis.[8]Currie BJ. Melioidosis: evolving concepts in epidemiology, pathogenesis and treatment. Semin Respir Crit Care Med. 2015;36:111-125.
https://www.thieme-connect.com/products/ejournals/html/10.1055/s-0034-1398389
http://www.ncbi.nlm.nih.gov/pubmed/25643275?tool=bestpractice.com
[92]Cheng AC, Limmathurotsakul D, Chierakul W, et al. A randomized controlled trial of granulocyte colony-stimulating factor for the treatment of severe sepsis due to melioidosis in Thailand. Clin Infect Dis. 2007;45:308-314.
http://cid.oxfordjournals.org/content/45/3/308.long
http://www.ncbi.nlm.nih.gov/pubmed/17599307?tool=bestpractice.com
[93]Cheng AC, Fisher DA, Anstey NM, et al. Outcomes of patients with melioidosis treated with meropenem. Antimicrob Agents Chemother. 2004;48:1763-1765.
http://aac.asm.org/content/48/5/1763.long
http://www.ncbi.nlm.nih.gov/pubmed/15105132?tool=bestpractice.com